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QDPR Polyclonal Antibody Reactivity Human

SKU: E-AB-52713-200

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QDPR Polyclonal Antibody Reactivity Human

 

SKU # E-AB-52713
Reactivity Human, Mouse, Rat
Host Rabbit
Applications WB, IHC

 

Product Details

Isotype IgG
Host Rabbit
Reactivity Human, Mouse, Rat
Applications WB, IHC
Clonality Polyclonal
Immunogen Fusion protein of human QDPR
Abbre QDPR
Synonyms member 1,  6,  7 dihydropteridine reductase,  DHPR,  Dihydropteridine reductase,  HDHPR,  HPR,  PKU2,  Qdpr,  Quinoid dihydropteridine reductase,  SDR33C1,  Short chain dehydrogenase/reductase family 33C
Swissprot
Calculated MW 26 kDa
Observed MW Refer to figures
Concentration 1.2 mg/mL
Buffer Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
Purification Method Antigen affinity purification
Research Areas Metabolism,  Signal transduction
Conjugation Unconjugated
Storage Store at -20°C Valid for 12 months. Avoid freeze / thaw cycles.
Shipping The product is shipped with ice pack, upon receipt, store it immediately at the temperature recommended.

 

Related Reagents

Applications Recommended Dilution
WB 1:500-1:2000
IHC 1:50-1:200

 

Background

This gene encodes the enzyme dihydropteridine reductase, which catalyzes the NADH-mediated reduction of quinonoid dihydrobiopterin. This enzyme is an essential component of the pterin-dependent aromatic amino acid hydroxylating systems. Mutations in this gene resulting in QDPR deficiency include aberrant splicing, amino acid substitutions, insertions, or premature terminations. Dihydropteridine reductase deficiency presents as atypical phenylketonuria due to insufficient production of biopterin, a cofactor for phenylalanine hydroxylase.